faculty

Publications

Case Report Management of pseudo tumour in haemophilia patients

Groups and Associations Sherlyn Ambrose1*, Giridhar Ashwath1, Sreekar Balasundaram2, Suresh Kumar2, Cecil Ross3, Anthony Prakash Rozario1
International Surgery Journal 2020

A hemophilic pseudotumor is one of the rare complications of hemophilia that results from repetitive bleeding,forming an expanding destructive encapsulated hematoma and necrosed tissue. It has a considerable amount ofmorbidity. These have become rare over the years with better treatment modalities like factor replacement. Presently,excision is the preferred treatment by many authors. There are instances where surgical excision is not feasible. In

such situations, radiotherapy and arterial embolization should be considered either alone or as an adjunct to surgery.A 32 years old male patient, with severe hemophilia A diagnosed with an abdominal tumour 7 years ago during

routine screening, that progressively grew to encompass the lower abdominal area. A 44 years old male patient withhemophilia A presented with slow growing swelling over the left gluteal region since, 10 years associated with

ulceration and bleeding since, 3 days. The management of a patient with a haemophilic pseudo tumour is complex,with a high rate of potential complications. Surgical excision is the treatment of choice but can only be carried out by

a multidisciplinary surgical team. The main postoperative complications are rebleed, infection, fistula andpathological fractures. Pelvic pseudo tumours can even become complicated by fistula formation to the large bowel

and by obstruction of the ureters. Untreated pseudo tumours will ultimately destroy soft tissues, erode bone, and mayproduce neurovascular complications. The hemophilic pseudo tumour is a rare entity which is slow growing painless

tumour, with few reports worldwide in the management of this rare complication